[Sildenafil treatment of unilateral pulmonary edema and pulmonary hypertension in pulmonary artery agenesis].

Congenital pulmonary artery agenesis is a rare cardiovascular malformation, frequently oligosymptomatic,1,2 that can be complicated with unilateral pulmonary edema3 or pulmonary hypertension.1,2,4 We report the case of a patient with congenital pulmonary artery agenesis and pulmonary hypertension who developed unilateral pulmonary edema and discuss the role of sildenafil in pulmonary hypertension. A 47-year-old woman, smoker of 20 cigarettes/day, with recurrent pulmonary infections, consulted for a hypertensive crisis. The physical examination was normal. The hemogram, biochemistry, coagulation tests, and electrocardiogram showed no alterations; there was mild hypoxemia in the arterial blood gas study. The chest x-ray revealed right pulmonary hyperlucency and a prominent left pulmonary artery. The echocardiogram showed concentric left ventricular hypertrophy Letters to the Editor